Rigid spine syndrome.

نویسندگان

  • I Goto
  • S Nagasaka
  • H Nagara
  • Y Kuroiwa
چکیده

A patient is described with distinctive clinical features including childhood onset of non-progressive muscle weakness, limitation of flexion of the neck and spine, scoliosis, and joint contracture. Muscle biopsy and electromyography showed findings suggestive of a myopathic disorder. The combination of these distinctive clinical features is termed the rigid spine syndrome. Only six cases have been reported in the literature to date.

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عنوان ژورنال:
  • Journal of neurology, neurosurgery, and psychiatry

دوره 42 3  شماره 

صفحات  -

تاریخ انتشار 1979